Pulmonary Hypertension in Adults with Congenital Heart Disease (ACHD) - Novel Aspects from the 7th World Symposium on Pulmonary Hypertension 2024 Pulmonale Hypertonie bei Erwachsenen mit angeborenen Herzfehlern (EMAH) – neue Aspekte vom 7. Weltsymposium zu Pulmonaler Hypertonie 2024

Huntgeburth M, Kaemmerer-Suleiman AS, Hager A, Lammers AE, Apitz C, von Scheidt F, Schmidt KH, Suleiman M, Kaemmerer H (2025)

Publication Type: Journal article, Review article

Publication year: 2025

Journal

Pneumologie Georg Thieme Verlag

Book Volume: 79

Pages Range: 831-842

Journal Issue: 10

DOI: 10.1055/a-2625-5000

Abstract

The number of adults with congenital heart defects (ACHD, CHD) is constantly rising, with more than 360,000 affected individuals in Germany and 50 million worldwide. Many patients with congenital heart defects (CHD) develop pulmonary hypertension (PH), often as pulmonary arterial hypertension (PAH) associated with congenital heart defects (P[A]H-CHD). P(A)H-CHD may occur early in life or develop long-term, even decades after repair, which is associated with significant morbidity and mortality. Due to the anatomical and hemodynamic complexity of CHD, PH in this population, especially among ACHD, often requires a more differentiated nuanced approach to diagnosis and treatment compared to most forms of PH. The European society of Cardiology (ESC) guidelines provide diagnostic and treatment approaches to P(A)H-CHD, but do not cover all aspects. The current contributions from the 7th World Symposium on Pulmonary Hypertension (7th WSPH, Barcelona 2024) provides an update of the diagnosis and an overview of the optimization of PH treatment to improve care of affected individuals, but primarily focuses on children and adolescents with CHD, while recommendations for adults with P(A)H-CHD are scarce. This article comments on specific aspects covering all contents of the 7th WSPH, in the context of existing guidelines, as well as regarding gaps in recommendations and future perspectives from the standpoint of congenital cardiology for ACHD.

Authors with CRIS profile

Ann-Sophie Kaemmerer-Suleiman Department of Cardiac Surgery Mathieu Suleiman Department of Cardiac Surgery

Involved external institutions

Technische Universität München (TUM) DE Germany (DE) Universitätsklinikum Münster DE Germany (DE) Universitätsklinikum Ulm DE Germany (DE) Universitätsmedizin der Johannes Gutenberg-Universität Mainz DE Germany (DE)

How to cite

APA:

Huntgeburth, M., Kaemmerer-Suleiman, A.-S., Hager, A., Lammers, A.E., Apitz, C., von Scheidt, F.,... Kaemmerer, H. (2025). Pulmonary Hypertension in Adults with Congenital Heart Disease (ACHD) - Novel Aspects from the 7th World Symposium on Pulmonary Hypertension 2024 Pulmonale Hypertonie bei Erwachsenen mit angeborenen Herzfehlern (EMAH) – neue Aspekte vom 7. Weltsymposium zu Pulmonaler Hypertonie 2024. Pneumologie, 79(10), 831-842. https://doi.org/10.1055/a-2625-5000

MLA:

Huntgeburth, Michael, et al. "Pulmonary Hypertension in Adults with Congenital Heart Disease (ACHD) - Novel Aspects from the 7th World Symposium on Pulmonary Hypertension 2024 Pulmonale Hypertonie bei Erwachsenen mit angeborenen Herzfehlern (EMAH) – neue Aspekte vom 7. Weltsymposium zu Pulmonaler Hypertonie 2024." Pneumologie 79.10 (2025): 831-842.

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