Consensus statement on the diagnosis and treatment of sclerosing diseases of the skin, Part 1: Localized scleroderma, systemic sclerosis and overlap syndromes

Knobler R, Geroldinger-Simić M, Kreuter A, Hunzelmann N, Moinzadeh P, Rongioletti F, Denton CP, Mouthon L, Cutolo M, Smith V, Gabrielli A, Bagot M, Olesen AB, Foeldvari I, Jalili A, Kähäri V, Kárpáti S, Kofoed K, Olszewska M, Panelius J, Quaglino P, Seneschal J, Sticherling M, Sunderkötter C, Tanew A, Wolf P, Worm M, Skrok A, Rudnicka L, Krieg T (2024)

Publication Type: Journal article

Publication year: 2024

Journal

DOI: 10.1111/jdv.19912

Abstract

The term ‘sclerosing diseases of the skin’ comprises specific dermatological entities, which have fibrotic changes of the skin in common. These diseases mostly manifest in different clinical subtypes according to cutaneous and extracutaneous involvement and can sometimes be difficult to distinguish from each other. The present consensus provides an update to the 2017 European Dermatology Forum Guidelines, focusing on characteristic clinical and histopathological features, diagnostic scores and the serum autoantibodies most useful for differential diagnosis. In addition, updated strategies for the first- and advanced-line therapy of sclerosing skin diseases are addressed in detail. Part 1 of this consensus provides clinicians with an overview of the diagnosis and treatment of localized scleroderma (morphea), and systemic sclerosis including overlap syndromes.

Authors with CRIS profile

Involved external institutions

Medizinische Universität Wien Austria (AT) Universität zu Köln Germany (DE) Ordensklinikum Linz - Elisabethinen Austria (AT) Turku University Hospital / Turun yliopistollinen keskussairaala (TYKS) Finland (FI) Wrocław Medical University / Uniwersytet Medyczny we Wrocławiu Poland (PL) Universität Witten/Herdecke Germany (DE) Helsingin yliopisto / University of Helsinki Finland (FI) University of Turin / Università degli Studi di Torino (UNITO) Italy (IT) Centre Hospitalier Universitaire de Bordeaux / CHU Bordeaux France (FR) Universitätsklinikum Halle (Saale) Germany (DE) Medizinische Universität Graz Austria (AT) Charité - Universitätsmedizin Berlin Germany (DE) Ospedale San Raffaele (früher: Centro San Raffaele del Monte Tabor Foundation) Italy (IT) UCL Medical School United Kingdom (GB) Hôpital Cochin France (FR) University of Genova / Università degli Studi di Genova Italy (IT) Universiteit Gent (UGent) / Ghent University Belgium (BE) Università Politecnica delle Marche (UNIVPM) / Marche Polytechnic University Italy (IT) Université Sorbonne Paris Cité France (FR) Aarhus University Hospital / Aarhus Universitetshospital Denmark (DK) Schön Klinik Hamburg Eilbek Germany (DE) Semmelweis University / Semmelweis Egyetem Hungary (HU) Dermatology & Skin Care Clinic Switzerland (CH)

How to cite

APA:

Knobler, R., Geroldinger-Simić, M., Kreuter, A., Hunzelmann, N., Moinzadeh, P., Rongioletti, F.,... Krieg, T. (2024). Consensus statement on the diagnosis and treatment of sclerosing diseases of the skin, Part 1: Localized scleroderma, systemic sclerosis and overlap syndromes. Journal of the European Academy of Dermatology and Venereology. https://doi.org/10.1111/jdv.19912

MLA:

Knobler, R., et al. "Consensus statement on the diagnosis and treatment of sclerosing diseases of the skin, Part 1: Localized scleroderma, systemic sclerosis and overlap syndromes." Journal of the European Academy of Dermatology and Venereology (2024).

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