Clinical characteristics and outcomes of children with WAGR syndrome and Wilms tumor and/or nephroblastomatosis: The 30-year SIOP-RTSG experience
Hol JA, Jongmans MCJ, Sudour-Bonnange H, Ramirez-Villar GL, Chowdhury T, Rechnitzer C, Pal N, Schleiermacher G, Karow A, Kuiper RP, De Camargo B, Avcin S, Redzic D, Wachtel A, Segers H, Vujanic GM, Van Tinteren H, Bergeron C, Pritchard-Jones K, Graf N, Van Den Heuvel-Eibrink MM (2020)
Publication Type: Journal article
Publication year: 2020
Journal
DOI: 10.1002/cncr.33304
Abstract
Background WAGR syndrome (Wilms tumor, aniridia, genitourinary anomalies, and range of developmental delays) is a rare contiguous gene deletion syndrome with a 45% to 60% risk of developing Wilms tumor (WT). Currently, surveillance and treatment recommendations are based on limited evidence.
Involved external institutions
Ljubljana University Medical Centre (Ljubljana UMC) / Univerzitetni klinični center Ljubljana
Slovenia (SI)
University College London (UCL)
United Kingdom (GB)
Princess Máxima Center
Netherlands (NL)
Rigshospitalet
Denmark (DK)
Sidra Medical and Research Center
Qatar (QA)
University Hospital Leuven (UZ) / Universitaire ziekenhuizen Leuven
Belgium (BE)
Instituto Nacional de Enfermedades Neoplásicas (INEN)
Peru (PE)
Centre Léon-Bérard (UNICANCER)
France (FR)
Institut Curie
France (FR)
Netherlands Cancer Institute (NKI)
Netherlands (NL)
Centre Oscar Lambret (UNICANCER)
France (FR)
National Cancer Institute (INCA)
Brazil (BR)
Hospitales Universitarios Virgen Macarena y Virgen del Rocío
Spain (ES)
Universität des Saarlandes (UdS)
Germany (DE)
Karolinska University Hospital / Karolinska Universitetssjukhuset
Sweden (SE)
Institut za Zdravstvenu Zastitu Majke i Deteta / Институт за здравствену заштиту мајке и детета Србије "Др Вукан Чупић"
Serbia (RS)
Slovenia (SI)
University College London (UCL)
United Kingdom (GB)
Princess Máxima Center
Netherlands (NL)
Rigshospitalet
Denmark (DK)
Sidra Medical and Research Center
Qatar (QA)
University Hospital Leuven (UZ) / Universitaire ziekenhuizen Leuven
Belgium (BE)
Instituto Nacional de Enfermedades Neoplásicas (INEN)
Peru (PE)
Centre Léon-Bérard (UNICANCER)
France (FR)
Institut Curie
France (FR)
Netherlands Cancer Institute (NKI)
Netherlands (NL)
Centre Oscar Lambret (UNICANCER)
France (FR)
National Cancer Institute (INCA)
Brazil (BR)
Hospitales Universitarios Virgen Macarena y Virgen del Rocío
Spain (ES)
Universität des Saarlandes (UdS)
Germany (DE)
Karolinska University Hospital / Karolinska Universitetssjukhuset
Sweden (SE)
Institut za Zdravstvenu Zastitu Majke i Deteta / Институт за здравствену заштиту мајке и детета Србије "Др Вукан Чупић"
Serbia (RS)
How to cite
APA:
Hol, J.A., Jongmans, M.C.J., Sudour-Bonnange, H., Ramirez-Villar, G.L., Chowdhury, T., Rechnitzer, C.,... Van Den Heuvel-Eibrink, M.M. (2020). Clinical characteristics and outcomes of children with WAGR syndrome and Wilms tumor and/or nephroblastomatosis: The 30-year SIOP-RTSG experience. Cancer. https://dx.doi.org/10.1002/cncr.33304
MLA:
Hol, Janna A., et al. "Clinical characteristics and outcomes of children with WAGR syndrome and Wilms tumor and/or nephroblastomatosis: The 30-year SIOP-RTSG experience." Cancer (2020).
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