Can stapedius reflex testing objectively measure muscle function in Pompe patients?

Hilz MJ, Hoppe U, Möller S, Wang R, Koehn J (2015)

Publication Type: Journal article

Publication year: 2015

Journal

Clinical Case Reports Wiley

Book Volume: 3

Pages Range: 937-41

Journal Issue: 11

DOI: 10.1002/ccr3.400

Abstract

We assessed the value of stapedius reflex testing as an objective measurement of striated muscle function in four patients with Pompe disease. Common tests of disease severity and efficacy of enzyme replacement therapy (ERT) yield highly variable results that depend on patient cooperation and day-to-day performance, whereas stapedius reflex thresholds improved in seven of eight ears after 2 years of ERT.

Authors with CRIS profile

Max-Josef Hilz Heisenbergprofessur für Neuroimmunologie Ulrich Hoppe Professur für Audiologie Sebastian Möller Department of Neurology Ruihao Wang Heisenbergprofessur für Neuroimmunologie

How to cite

APA:

Hilz, M.-J., Hoppe, U., Möller, S., Wang, R., & Koehn, J. (2015). Can stapedius reflex testing objectively measure muscle function in Pompe patients? Clinical Case Reports, 3(11), 937-41. https://doi.org/10.1002/ccr3.400

MLA:

Hilz, Max-Josef, et al. "Can stapedius reflex testing objectively measure muscle function in Pompe patients?" Clinical Case Reports 3.11 (2015): 937-41.

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