Progressive skin fibrosis is associated with a decline in lung function and worse survival in patients with diffuse cutaneous systemic sclerosis in the European Scleroderma Trials and Research (EUSTAR) cohort

Wu W, Jordan S, Graf N, Pena JDO, Curram J, Allanore Y, Matucci-Cerinic M, Pope JE, Denton CP, Khanna D, Distler O, Matucci-Cerinic M, Guiducci S, Walker U, Jaeger V, Bannert B, Lapadula G, Becvarare R, Cutolo M, Valentini G, Siegert E, Rednic S, Allanore Y, Montecucco C, Carreira PE, Novak S, Czirjak L, Varju C, Chizzolini C, Allai D, Kucharz EJ, Cozzi F, Rozman B, Mallia C, Gabrielli A, Bancel DF, Airo P, Hesselstrand R, Martinovic D, Balbir-Gurman A, Braun-Moscovici Y, Hunzelmann N, Pellerito R, Caramaschi P, Black C, Damjanov N, Henes J, Ortiz Santamaria V, Heitmann S, Seidel M, Pereira Da Silva JA, Stamenkovic B, Selmi CF, Tikly M, Denisov LN, Mueller-Ladner U, Engelhart M, Hachulla E, Riccieri V, Ionescu RM, Mihai C, Sunderkoetter C, Kuhn A, Schett G, Distler J, Meroni P, Ingegnoli F, Mouthon L, De Keyser F, Smith V, Cantatore FP, Corrado A, Ullman S, Iversen L, Pozzi MR, Eyerich K, Hein R, Knott E, Wiland P, Szmyrka-Kaczmarek M, Sokolik R, Morgiel E, Madej M, Jose Alegre-Sancho J, Krummel-Lorenz B, Saar P, Aringer M, Günther C, Anne E, Westhovens R, De Langhe E, Lenaerts J, Anic B, Baresic M, Mayer M, Uprus M, Otsa K, Yavuz S, Radominski SC, Mueller CDS, Azevedo VF, Popa S, Zenone T, Stebbings S, Highton J, Mathieu A, Vacca A, Stamp L, Chapman P, O'Donnell J, Solanki K, Doube A, Veale D, O'Rourke M, Loyo E, Li M, Rosato E, Amoroso A, Gigante A, Oksel F, Yargucu F, Tanaseanu CM, Popescu M, Dumitrascu A, Tiglea I, Foti R, Visalli E, Benenati A, Amato G, Ancuta C, Chirieac R, Villiger P, Adler S, Dan D, De La Pena Lefebvre PG, Rodriguez Rubio S, Valero Exposito M, Sibilia J, Chatelus E, Gottenberg JE, Chifflot H, Litinsky I, Del Galdo F, Venalis A, Saketkoo LA, Lasky JA, Kerzberg E, Montoya F, Cosentino V, Limonta M, Brucato AL, Lupi E, Spertini F, Ribi C, Buss G, Martin T, Guffroy A, Poindron V, Chung L, Schmeiser T, Zebryk P, Riso N, Riemekasten G, Rezus E, Puttini PS (2019)


Publication Type: Journal article

Publication year: 2019

Journal

Book Volume: 78

Pages Range: 648-656

Journal Issue: 5

DOI: 10.1136/annrheumdis-2018-213455

Abstract

Objectives To determine whether progressive skin fibrosis is associated with visceral organ progression and mortality during follow-up in patients with diffuse cutaneous systemic sclerosis (dcSSc).

Authors with CRIS profile

Involved external institutions

Spitalul Clinic Dr. I. Cantacuzino RO Romania (RO) Bayer Plc GB United Kingdom (GB) Geneva University Hospitals / Hôpitaux universitaires de Genève (HUG) CH Switzerland (CH) Bayer Corporation US United States (USA) (US) Universitätsspital Zürich (USZ) CH Switzerland (CH) Universität Bern CH Switzerland (CH) Hôpital civil FR France (FR) Azienda Ospedaliera San Gerardo (ASST Monza) IT Italy (IT) Università degli Studi di Firenze / University of Florence IT Italy (IT) Universitätsspital Basel CH Switzerland (CH) University College London (UCL) GB United Kingdom (GB) University of Michigan US United States (USA) (US) KBC Rijeka HR Croatia (HR) University of Genova / Università degli Studi di Genova IT Italy (IT) University of Pécs / Pécsi Tudományegyetem HU Hungary (HU) University of Bari Aldo Moro / Università degli Studi di Bari Aldo Moro IT Italy (IT) Technische Universität München (TUM) DE Germany (DE) Ospedale Liriuniti IT Italy (IT) Iuliu Hațieganu University of Medicine and Pharmacy / Universitatea de Medicină și Farmacie "Iuliu Hațieganu" (UMF Cluj) RO Romania (RO) graf biostatistics CH Switzerland (CH) Grigore T. Popa University of Medicine and Pharmacy / Universitatea de Medicină și Farmacie "Grigore T. Popa" (UMF Iași) RO Romania (RO) Krankenhaus St. Josef DE Germany (DE) Ljubljana University Medical Centre (Ljubljana UMC) / Univerzitetni klinični center Ljubljana SI Slovenia (SI) Universitätsklinikum Köln DE Germany (DE) University Hospital Split HR Croatia (HR) Marienhospital Stuttgart DE Germany (DE) Skåne University Hospital / Skånes universitetssjukhus SE Sweden (SE) L'Ospedale Mauriziano di Torino IT Italy (IT) Universidade de Coimbra PT Portugal (PT) Universitätsklinikum Heidelberg DE Germany (DE) Assistance Publique-Hôpitaux de Paris (AP-HP) FR France (FR) V.A. Nasonova Research Institute of Rheumatology RU Russian Federation (RU) Hospital Clínico Universitario de Valencia ES Spain (ES) Universidade Federal do Paraná (UFPR) BR Brazil (BR) Marmara University TR Turkey (TR) Technische Universität Dresden DE Germany (DE) Gentofte Hospital DK Denmark (DK) Kerckhoff-Klinik DE Germany (DE) University Hospital Leuven (UZ) / Universitaire ziekenhuizen Leuven BE Belgium (BE) Azienda Ospedaliero Universitaria "Policlinico - Vittorio Emanuele" IT Italy (IT) Wrocław Medical University / Uniwersytet Medyczny we Wrocławiu PL Poland (PL) University of Zagreb / Sveučilište u Zagrebu HR Croatia (HR) St Vincent's University Hospital IE Ireland (IE) Copenhagen University Hospital DK Denmark (DK) University of Otago NZ New Zealand (NZ) Università degli studi "La Sapienza" IT Italy (IT) Università degli Studi di Cagliari IT Italy (IT) Westfälische Wilhelms-Universität (WWU) Münster DE Germany (DE) University of Waikato NZ New Zealand (NZ) Ege University / Ege Üniversitesi TR Turkey (TR) Spitalul Clinic de Urgenta "Sf. Pantelimon" RO Romania (RO) Hôpital Cochin FR France (FR) Timofei Moșneaga Republican Clinical Hospital MD Moldova, Republic of (MD) Universitätsklinikum Schleswig-Holstein (UKSH) DE Germany (DE) Hospital Curry Cabral PT Portugal (PT) Poznan University of Medical Sciences / Uniwersytet Medyczny im. Karola Marcinkowskiego w Poznaniu PL Poland (PL) Hôpitaux universitaires de Strasbourg (HUS) / University Hospital Strasbourg FR France (FR) Hospital Universitario HM Sanchinarro ES Spain (ES) University of Leeds GB United Kingdom (GB) Tel Aviv Sourasky Medical Center / Ichilov Hospital IL Israel (IL) Universidad de Buenos Aires (UBA) / University of Buenos Aires AR Argentina (AR) Tulane University US United States (USA) (US) Azienda Socio Sanitaria Territoriale degli Spedali Civili di Brescia IT Italy (IT) University of Foggia / Università degli studi di Foggia IT Italy (IT) Hôpital Claude Huriez FR France (FR) Universiteit Gent (UGent) / Ghent University BE Belgium (BE) Univerzita Karlova v Praze / Charles University in Prague CZ Czech Republic (CZ) University of Paris 5 - René Descartes / Université Paris V René Descartes FR France (FR) Università degli studi di Milano IT Italy (IT) Hospital Jose Maria Cabral Y Baez DO Dominican Republic (DO) Royal Free Hospital GB United Kingdom (GB) Institute of Rheumatology / Institut za Reumatologiju RS Serbia (RS) Università Politecnica delle Marche (UNIVPM) / Marche Polytechnic University IT Italy (IT) Stanford University US United States (USA) (US) Peking Union Medical College / 北京协和医学院 CN China (CN) University of Verona / Università degli Studi di Verona IT Italy (IT) Rambam Health Care Campus IL Israel (IL) East Tallinn Central Hospital EE Estonia (EE) Medical University of Silesia in Katowice / Śląski Uniwersytet Medyczny w Katowicach (SUM) PL Poland (PL) University of Padua / Universita degli Studi di Padova IT Italy (IT) Hospital General de Granollers ES Spain (ES) Western University CA Canada (CA) Universitätsklinikum Bonn DE Germany (DE) Luigi Sacco Hospital IT Italy (IT) Charité - Universitätsmedizin Berlin DE Germany (DE) Hospital Universitario 12 de Octubre ES Spain (ES) Policlinico San Matteo Pavia Fondazione IRCCS IT Italy (IT) Institut Niška Banja RS Serbia (RS) Chris Hani Baragwanath Hospital ZA South Africa (ZA) Carol Davila University of Medicine and Pharmacy / Universitatea de Medicină și Farmacie „Carol Davila” (UMF București) RO Romania (RO) Universitätsklinikum Carl Gustav Carus Dresden DE Germany (DE)

How to cite

APA:

Wu, W., Jordan, S., Graf, N., Pena, J.D.O., Curram, J., Allanore, Y.,... Puttini, P.S. (2019). Progressive skin fibrosis is associated with a decline in lung function and worse survival in patients with diffuse cutaneous systemic sclerosis in the European Scleroderma Trials and Research (EUSTAR) cohort. Annals of the Rheumatic Diseases, 78(5), 648-656. https://dx.doi.org/10.1136/annrheumdis-2018-213455

MLA:

Wu, Wanlong, et al. "Progressive skin fibrosis is associated with a decline in lung function and worse survival in patients with diffuse cutaneous systemic sclerosis in the European Scleroderma Trials and Research (EUSTAR) cohort." Annals of the Rheumatic Diseases 78.5 (2019): 648-656.

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